In order to benchmark the performance of the algorithms, 227 OMIM phenotypes that were linked to more than one gene (i.e.mutations in different genes that produce the same phenotype) were selected from the EntrezGene database.
For each disease, we fixed one gene as the "target gene". Then, to do the predictions, we defined a chromosomal region of 30 Mb around
the target gene. All the tested methods use different inputs
but the predictions were made in the same bands around the target genes.
| OMIM |
DISEASE NAME |
TARGET GENE |
TARGET GENE NAME |
Chr |
From |
To |
ADDITIONAL GENES |
| 101400 |
Saethre-Chotzen syndrome with eyelid anomalies |
2263 |
FGFR2 fibroblast growth factor receptor 2 isoform 1 |
chr10 | 105413628 | 135413628 |
7291
|
| 102200 |
Acromelagy |
2778 |
GNAS guanine nucleotide binding protein, alpha |
chr20 | 32435964 | 62435964 |
6755
|
| 103470 |
Waardenburg syndrome/albinism, digenic |
4286 |
MITF microphthalmia-associated transcription factor |
chr3 | 55082826 | 85082826 |
7299
|
| 103780 |
Alcoholism, susceptibility to |
2555 |
GABRA2 gamma-aminobutyric acid A receptor, alpha 2 |
chr4 | 31162451.5 | 61162451.5 |
3356
|
| 104300 |
Alzheimer disease 6 |
323 |
APBB2 amyloid beta A4 precursor protein-binding, |
chr4 | 25767617.5 | 55767617.5 |
1636
4353
4846
5328
22976
|
| 105150 |
Cerebral amyloid angiopathy |
19 |
ABCA1 ATP-binding cassette, sub-family A member 1 |
chr9 | 89685832.5 | 119685832.5 |
1471
|
| 105200 |
Amyloidosis, hereditary renal |
2243 |
FGA fibrinogen, alpha chain isoform alpha |
chr4 | 140866847 | 170866847 |
4069
|
| 105400 |
Amyotrophic lateral sclerosis |
1639 |
DCTN1 dynactin 1 isoform 2 |
chr2 | 59506707 | 89506707 |
4744
5630
6647
|
| 105830 |
Angelman syndrome |
4204 |
MECP2 methyl CpG binding protein 2 |
chrX | 124824264 | 154824264 |
7337
|
| 107250 |
Anterior segment mesenchymal dysgenesis and cataract |
2301 |
FOXE3 forkhead box E3 |
chr1 | 32594487 | 62594487 |
5309
|
| 109800 |
Bladder cancer |
2261 |
FGFR3 fibroblast growth factor receptor 3 isoform 1 |
chr4 | 0 | 30000000 |
3265
3845
5925
|
| 111400 |
Blood group, P system |
8706 |
B3GALT3 UDP-Gal:betaGlcNAc beta |
chr3 | 147286746 | 177286746 |
53947
|
| 113800 |
Epidermolytic hyperkeratosis |
3848 |
KRT1 keratin 1 |
chr12 | 36357821 | 66357821 |
3858
|
| 114030 |
Cafe-au-lait spots with glioma or leukemia |
4292 |
MLH1 MutL protein homolog 1 |
chr3 | 22038595 | 52038595 |
4436
|
| 114480 |
Breast cancer |
472 |
ATM ataxia telangiectasia mutated protein isoform 2 |
chr11 | 92702516 | 122702516 |
580
675
3845
5002
5290
5888
7157
8493
9821
11200
83990
|
| 114500 |
Colon cancer, hereditary nonpolypopsis |
701 |
BUB1B BUB1 budding uninhibited by benzimidazoles 1 |
chr15 | 23270482.5 | 53270482.5 |
2033
4953
5157
5290
5320
5795
7157
8313
27030
201163
|
| 114550 |
Hepatocellular cancer |
841 |
CASP8 caspase 8 isoform C |
chr2 | 186966769 | 216966769 |
1499
4233
5157
7157
8312
|
| 115200 |
Cardiomyopathy, dilated |
70 |
ACTC cardiac muscle alpha actin proprotein |
chr15 | 17872102.5 | 47872102.5 |
4000
4625
5350
|
| 120200 |
Coloboma, ocular |
5080 |
PAX6 paired box gene 6 isoform a |
chr11 | 16776296 | 46776296 |
6469
|
| 122000 |
Corneal dystrophy, posterior polymorphous |
1296 |
COL8A2 collagen, type VIII, alpha 2 |
chr1 | 21233599 | 51233599 |
30813
|
| 122100 |
Meesmann corneal dystrophy |
3850 |
KRT3 keratin 3 |
chr12 | 36473092.5 | 66473092.5 |
3859
|
| 122700 |
Coumarin resistance |
1548 |
CYP2A6 cytochrome P450, family 2, subfamily A, |
chr19 | 31044855.5 | 61044855.5 |
1559
79001
|
| 123150 |
Jackson-Weiss sydnrome |
2260 |
FGFR1 fibroblast growth factor receptor 1 isoform 1 |
chr8 | 23412211.5 | 53412211.5 |
2263
|
| 123700 |
Cutis laxa |
2006 |
ELN elastin |
chr7 | 57907424 | 87907424 |
10516
|
| 124000 |
Mitochondrial complex III deficiency |
617 |
BCS1L BCS1-like |
chr2 | 204352414.5 | 234352414.5 |
7381
|
| 125850 |
MODY, one form |
3172 |
HNF4A hepatocyte nuclear factor 4 alpha isoform f |
chr20 | 27452144.5 | 57452144.5 |
3630
|
| 125853 |
Diabetes mellitus, noninsulin-dependent |
208 |
AKT2 v-akt murine thymoma viral oncogene homolog 2 |
chr19 | 30447316 | 60447316 |
2642
2820
3172
3651
4760
5167
6833
6927
6928
7422
8660
9479
56729
|
| 126200 |
Multiple sclerosis, susceptibility to |
4261 |
CIITA class II transactivator |
chr16 | 0 | 30000000 |
5788
|
| 127750 |
Dementia, Lewy body |
6620 |
SNCB beta-synuclein |
chr5 | 150857866 | 180857866 |
6622
|
| 130000 |
Ehlers-Danlos syndrome, type I |
1277 |
COL1A1 alpha 1 type I collagen preproprotein |
chr17 | 30625867 | 60625867 |
1289
1290
|
| 130020 |
Ehlers-Danlos syndrome, type III |
1281 |
COL3A1 procollagen, type III, alpha 1 |
chr2 | 174683363.5 | 204683363.5 |
7148
|
| 130060 |
Ehlers-Danlos syndrome, type VII |
1277 |
COL1A1 alpha 1 type I collagen preproprotein |
chr17 | 30625867 | 60625867 |
1278
|
| 130650 |
Beckwith-Wiedemann syndrome |
1028 |
CDKN1C cyclin-dependent kinase inhibitor 1C |
chr11 | 0 | 30000000 |
64324
|
| 131800 |
Epidermolysis bullosa simplex, Koebner, Dowling-Meara, and Weber-Cockayne types |
3691 |
ITGB4 integrin beta 4 isoform 3 precursor |
chr17 | 48774742 | 78774742 |
3852
3861
|
| 132600 |
Pilomatrixoma |
1499 |
CTNNB1 catenin (cadherin-associated protein), beta 1, |
chr3 | 26248200 | 56248200 |
4595
|
| 133200 |
Erythrokeratodermia variabilis with erythema gyratum repens |
2707 |
GJB3 connexin 31 |
chr1 | 19919862.5 | 49919862.5 |
127534
|
| 133239 |
Esophageal cancer |
6049 |
RNF6 ring finger protein 6 isoform 1 |
chr13 | 10688873 | 40688873 |
7048
9940
11178
50514
51741
|
| 133780 |
Vitreoretinopathy, exudative, familial |
4041 |
LRP5 low density lipoprotein receptor-related protein |
chr11 | 52904936 | 82904936 |
8322
|
| 136880 |
Fundus albipunctatus |
5959 |
RDH5 retinol dehydrogenase 5 (11-cis and 9-cis) |
chr12 | 39402915.5 | 69402915.5 |
5961
6017
|
| 137215 |
Gastric cancer |
324 |
APC adenomatosis polyposis coli |
chr5 | 97163104 | 127163104 |
843
999
1316
2064
2263
3553
3557
3659
3845
4595
|
| 137750 |
Glaucoma 1A, primary open angle, juvenile-onset |
1545 |
CYP1B1 cytochrome P450, family 1, subfamily B, |
chr2 | 23211848.5 | 53211848.5 |
4010
4653
|
| 137760 |
Glaucoma 1B, primary open angle, adult onset |
1545 |
CYP1B1 cytochrome P450, family 1, subfamily B, |
chr2 | 23211848.5 | 53211848.5 |
10133
134430
|
| 137800 |
Glioblastoma multiforme, somatic |
1755 |
DMBT1 deleted in malignant brain tumors 1 isoform c |
chr10 | 105413628 | 135413628 |
2064
4436
5468
5728
9211
55717
|
| 142623 |
Hirschsprung disease |
1908 |
EDN3 endothelin 3 isoform 1 preproprotein |
chr20 | 32435964 | 62435964 |
2668
3897
4902
5979
8929
|
| 143465 |
Attention-deficit hyperactivity disorder, susceptibility to |
1816 |
DRD5 dopamine receptor D5 |
chr4 | 0 | 30000000 |
6531
|
| 143890 |
Hypercholesterolemia, familial |
19 |
ABCA1 ATP-binding cassette, sub-family A member 1 |
chr9 | 89685832.5 | 119685832.5 |
336
2053
3700
3949
10842
|
| 144200 |
Epidermolytic palmoplantar keratoderma |
3857 |
KRT9 keratin 9 |
chr17 | 21979410 | 51979410 |
3868
|
| 144700 |
Renal cell carcinoma |
4968 |
OGG1 8-oxoguanine DNA glycosylase isoform 1a |
chr3 | 0 | 30000000 |
11236
84925
201163
|
| 145000 |
Hyperparathyroidism, AD |
4221 |
MEN1 menin isoform 1 |
chr11 | 49331269 | 79331269 |
79577
|
| 145500 |
Hypertension, essential |
118 |
ADD1 adducin 1 (alpha) isoform a |
chr4 | 0 | 30000000 |
183
185
1577
1889
2784
4843
4846
5740
|
| 145750 |
Hypertriglyceridemia, susceptibility to |
6101 |
RP1 retinitis pigmentosa RP1 protein |
chr8 | 40700772.5 | 70700772.5 |
116519
149998
|
| 145900 |
Dejerine-Sottas disease |
1959 |
EGR2 early growth response 2 protein |
chr10 | 49244383.5 | 79244383.5 |
4359
5376
57716
|
| 146110 |
Hypogonadotropic hypogonadism |
26012 |
NELF nasal embryonic LHRH factor |
chr9 | 108429268 | 138429268 |
84634
|
| 146200 |
Hypoparathyroidism, familial |
846 |
CASR calcium-sensing receptor |
chr3 | 108471227 | 138471227 |
5741
9247
|
| 147050 |
Atopy |
2206 |
MS4A2 membrane-spanning 4-domains, subfamily A, member |
chr11 | 44616259.5 | 74616259.5 |
6403
7941
11005
26762
51131
|
| 148700 |
Keratosis palmoplantaris striata I |
1828 |
DSG1 desmoglein 1 preproprotein |
chr18 | 12170784 | 42170784 |
3848
|
| 149400 |
Startle disease/hyperekplexia, autosomal dominant |
2741 |
GLRA1 glycine receptor, alpha 1 |
chr5 | 136233364.5 | 166233364.5 |
2743
|
| 151400 |
Leukemia, chronic lymphatic, susceptibility to |
595 |
CCND1 cyclin D1 |
chr11 | 54170246.5 | 84170246.5 |
5027
115761
|
| 151623 |
Li Fraumeni syndrome |
1029 |
CDKN2A cyclin-dependent kinase inhibitor 2A isoform 1 |
chr9 | 6961526.5 | 36961526.5 |
7157
|
| 151660 |
Lipodystrophy, familial partial |
4000 |
LMNA lamin A/C isoform 3 |
chr1 | 137909876 | 167909876 |
5468
|
| 152700 |
Lupus erythematosus, systemic, susceptibility |
356 |
FASLG fas ligand |
chr1 | 154363405.5 | 184363405.5 |
1773
2214
5133
26191
|
| 155240 |
Medullary thyroid carcinoma |
4914 |
NTRK1 neurotrophic tyrosine kinase, receptor, type 1 |
chr1 | 138654153 | 168654153 |
5979
|
| 155255 |
Medulloblastoma |
29 |
ABR active breakpoint cluster region-related |
chr17 | 0 | 30000000 |
324
675
1499
1755
8643
51684
|
| 157300 |
Migraine with aura, susceptibility to |
1909 |
EDNRA endothelin receptor type A |
chr4 | 133792906.5 | 163792906.5 |
2099
7124
|
| 157640 |
Progressive external ophthalmoplegia with mitochondrial DNA deletions |
291 |
SLC25A4 solute carrier family 25 (mitochondrial carrier; |
chr4 | 161411218 | 191411218 |
5428
56652
|
| 158000 |
Monilethrix |
3887 |
KRTHB1 keratin, hair, basic, 1 |
chr12 | 35968910.5 | 65968910.5 |
3892
|
| 158350 |
Cowden disease |
657 |
BMPR1A bone morphogenetic protein receptor, type IA |
chr10 | 73649605.5 | 103649605.5 |
5728
|
| 158810 |
Bethlem myopathy |
1291 |
COL6A1 collagen, type VI, alpha 1 precursor |
chr21 | 16944323 | 46944323 |
1292
1293
|
| 159900 |
Dystonia, myoclonic |
1813 |
DRD2 dopamine receptor D2 isoform short |
chr11 | 97793620.5 | 127793620.5 |
8910
|
| 161800 |
Myopathy, nemaline |
58 |
ACTA1 alpha 1 actin precursor |
chr1 | 210874788.5 | 240874788.5 |
7169
7170
|
| 164230 |
Obsessive-compulsive disorder, protection against |
627 |
BDNF brain-derived neurotrophic factor isoform a |
chr11 | 12636315 | 42636315 |
3356
6532
|
| 165720 |
Osteoarthritis susceptibility, female-specifi |
1280 |
COL2A1 alpha 1 type II collagen isoform 2, |
chr12 | 31668913.5 | 61668913.5 |
2487
54829
|
| 166710 |
Osteopenia/osteoporosis |
799 |
CALCR calcitonin receptor |
chr7 | 77730631 | 107730631 |
1277
1278
3569
4041
8572
|
| 167200 |
Pachyonychia congenita, Jadassohn-Lewandowsky type |
3853 |
KRT6A keratin 6A |
chr12 | 36170504.5 | 66170504.5 |
3868
|
| 167210 |
Pachyonychia congenita, Jackson-Lawler type |
3854 |
KRT6B keratin 6B |
chr12 | 36129684.5 | 66129684.5 |
3872
|
| 167800 |
Pancreatitis, hereditary |
5644 |
PRSS1 protease, serine, 1 preproprotein |
chr7 | 126945392 | 156945392 |
6690
|
| 168000 |
Paragangliomas, familial central nervous system |
6390 |
SDHB succinate dehydrogenase complex, subunit B, iron |
chr1 | 2108250.5 | 32108250.5 |
6392
|
| 168500 |
Parietal foramina 1 |
4488 |
MSX2 msh homeobox 2 |
chr5 | 150857866 | 180857866 |
60529
|
| 168600 |
Parkinson disease |
1621 |
DBH dopamine beta-hydroxylase precursor |
chr9 | 108429268 | 138429268 |
4137
4729
4929
6908
7345
9627
|
| 170400 |
Hypokalemic periodic paralysis |
779 |
CACNA1S calcium channel, voltage-dependent, L type, |
chr1 | 182776869.5 | 212776869.5 |
6329
10008
|
| 171300 |
Pheochromocytoma |
6392 |
SDHD succinate dehydrogenase complex, subunit D |
chr11 | 96466872.5 | 126466872.5 |
7428
|
| 172700 |
Dementia, Pick disease-like |
4137 |
MAPT microtubule-associated protein tau isoform 3 |
chr17 | 26426460.5 | 56426460.5 |
5663
|
| 174050 |
Polycystic liver disease |
5589 |
PRKCSH protein kinase C substrate 80K-H isoform 2 |
chr19 | 0 | 30000000 |
11231
|
| 174900 |
Polyposis, juvenile intestinal |
657 |
BMPR1A bone morphogenetic protein receptor, type IA |
chr10 | 73649605.5 | 103649605.5 |
4089
|
| 176200 |
Porphyria variegata |
3077 |
HFE hemochromatosis protein isoform 10 precursor |
chr6 | 11199040 | 41199040 |
5498
|
| 176270 |
Prader-Willi syndrome |
4692 |
NDN necdin |
chr15 | 6482974 | 36482974 |
6638
|
| 176807 |
Prostate cancer 1 |
367 |
AR androgen receptor isoform 2 |
chrX | 51649284.5 | 81649284.5 |
463
675
1316
2048
3092
3732
4481
4601
5728
7991
8379
11200
60528
|
| 177200 |
Liddle syndrome |
6338 |
SCNN1B sodium channel, nonvoltage-gated 1, beta |
chr16 | 8283522 | 38283522 |
6340
|
| 178500 |
Pulmonary fibrosis, idiopathic, susceptibility to |
6435 |
SFTPA1 surfactant, pulmonary-associated protein A1 |
chr10 | 66362677 | 96362677 |
6440
|
| 180300 |
Rheumatoid arthritis, susceptibility to |
861 |
RUNX1 runt-related transcription factor 1 isoform b |
chr21 | 16944323 | 46944323 |
3586
4261
4795
6583
23569
26191
|
| 180800 |
Roussy-Levy syndrome |
4359 |
MPZ myelin protein zero |
chr1 | 143090768 | 173090768 |
5376
|
| 180849 |
Rubenstein-Taybi syndrome |
1387 |
CREBBP CREB binding protein |
chr16 | 0 | 30000000 |
2033
|
| 181000 |
Sarcoidosis, susceptibility to |
3123 |
HLA-DRB1 major histocompatibility complex, class II, DR |
chr6 | 17660171 | 47660171 |
56244
64127
|
| 181500 |
Schizophrenia |
207 |
AKT1 v-akt murine thymoma viral oncogene homolog 1 |
chr14 | 76368585 | 106368585 |
1312
1610
3356
6854
8542
23780
27185
65078
80832
84062
267012
|
| 182940 |
Spina bifida, risk of |
4548 |
MTR 5-methyltetrahydrofolate-homocysteine |
chr1 | 215522847 | 245522847 |
4552
|
| 187500 |
Tetralogy of Fallot |
182 |
JAG1 jagged 1 precursor |
chr20 | 0 | 30000000 |
1482
23414
|
| 187950 |
Thrombocythemia, essential |
3717 |
JAK2 Janus kinase 2 |
chr9 | 0 | 30000000 |
4352
7066
|
| 188470 |
Thyroid carcinoma, follicular |
3265 |
HRAS v-Ha-ras Harvey rat sarcoma viral oncogene |
chr11 | 0 | 30000000 |
5728
9562
|
| 188550 |
Thyroid carcinoma, papillary |
5108 |
PCM1 pericentriolar material 1 |
chr8 | 2883425 | 32883425 |
5573
8030
8031
8805
9950
51592
|
| 189800 |
Preeclampsia |
4846 |
NOS3 nitric oxide synthase 3 (endothelial cell) |
chr7 | 128628139 | 158628139 |
219736
|
| 190685 |
Down syndrome |
2623 |
GATA1 GATA binding protein 1 |
chrX | 33407292.5 | 63407292.5 |
4548
|
| 191100 |
Tuberous sclerosis-1 |
3458 |
IFNG interferon, gamma |
chr12 | 51837530.5 | 81837530.5 |
7248
7249
|
| 192600 |
Cardiomyopathy, familial hypertrophic, 1 |
70 |
ACTC cardiac muscle alpha actin proprotein |
chr15 | 17872102.5 | 47872102.5 |
859
4624
4625
85366
|
| 193300 |
Hemangioblastoma, cerebellar,somatic |
595 |
CCND1 cyclin D1 |
chr11 | 54170246.5 | 84170246.5 |
7428
|
| 193900 |
White sponge nevus |
3851 |
KRT4 keratin 4 |
chr12 | 36490614 | 66490614 |
3860
|
| 194070 |
Denys-Drash syndrome |
675 |
BRCA2 breast cancer 2, early onset |
chr13 | 16829752 | 46829752 |
2719
7490
|
| 201400 |
ACTH deficiency |
1392 |
CRH corticotropin releasing hormone precursor |
chr8 | 52251970.5 | 82251970.5 |
9095
|
| 202370 |
Adrenoleukodystrophy, neonatal |
5189 |
PEX1 peroxisome biogenesis factor 1 |
chr7 | 76781910.5 | 106781910.5 |
5192
5194
5830
55670
|
| 202400 |
Afibrinogenemia |
2243 |
FGA fibrinogen, alpha chain isoform alpha |
chr4 | 140866847 | 170866847 |
2244
|
| 202700 |
Neutropenia, congenital |
1991 |
ELA2 elastase 2, neutrophil preproprotein |
chr19 | 0 | 30000000 |
2672
|
| 203300 |
Hermansky-Pudlak syndrome |
3257 |
HPS1 Hermansky-Pudlak syndrome 1 protein isoform a |
chr10 | 85180148.5 | 115180148.5 |
11234
79803
84062
84343
89781
|
| 203450 |
Alexander disease |
2670 |
GFAP glial fibrillary acidic protein |
chr17 | 25344310 | 55344310 |
4723
|
| 203780 |
Alport syndrome, autosomal recessive |
1285 |
COL4A3 alpha 3 type IV collagen isoform 4, precursor |
chr2 | 212928488 | 242928488 |
1286
|
| 204000 |
Leber congenital amaurosis |
1406 |
CRX cone-rod homeobox protein |
chr19 | 33811651 | 63811651 |
3000
23418
57096
|
| 209880 |
Central hypoventilation syndrome, congenital |
627 |
BDNF brain-derived neurotrophic factor isoform a |
chr11 | 12636315 | 42636315 |
1908
2668
5979
8929
|
| 209900 |
Bardet-Biedl syndrome 1 |
582 |
BBS1 Bardet-Biedl syndrome 1 |
chr11 | 51045395 | 81045395 |
583
585
8195
55212
84100
123016
129880
|
| 209920 |
Bare lymphocyte syndrome, type II, complementation group C |
4261 |
CIITA class II transactivator |
chr16 | 0 | 30000000 |
5993
5994
8625
|
| 209950 |
BCG and salmonella infection, disseminated |
3459 |
IFNGR1 interferon gamma receptor 1 |
chr6 | 122571508.5 | 152571508.5 |
3460
3593
3594
6772
|
| 210250 |
Sitosterolemia |
64240 |
ABCG5 sterolin 1 |
chr2 | 28964687 | 58964687 |
64241
|
| 211900 |
Calcinosis, tumoral |
2591 |
GALNT3 polypeptide N-acetylgalactosaminyltransferase 3 |
chr2 | 151441757 | 181441757 |
8074
|
| 211980 |
Lung cancer |
673 |
BRAF v-raf murine sarcoma viral oncogene homolog B1 |
chr7 | 124982633.5 | 154982633.5 |
1326
1956
2064
3845
5002
5071
5519
9940
|
| 214100 |
Zellweger syndrome |
5189 |
PEX1 peroxisome biogenesis factor 1 |
chr7 | 76781910.5 | 106781910.5 |
5192
5194
5195
5824
5830
8504
55670
|
| 214150 |
Cerebrooculofacioskeletal syndrome |
2068 |
ERCC2 excision repair cross-complementing rodent |
chr19 | 33811651 | 63811651 |
2073
|
| 215600 |
Cirrhosis, noncryptogenic, susceptibility to |
3856 |
KRT8 keratin 8 |
chr12 | 36581255 | 66581255 |
3875
|
| 217095 |
Conotruncal cardiac anomalies |
6899 |
TBX1 T-box 1 isoform B |
chr22 | 3133409.5 | 33133409.5 |
55997
|
| 219000 |
Fraser syndrome |
80144 |
FRAS1 Fraser syndrome 1 isoform 4 |
chr4 | 64461375 | 94461375 |
341640
|
| 219050 |
Cryptorchidism, idiopathic |
3640 |
INSL3 insulin-like 3 precursor |
chr19 | 2790988.5 | 32790988.5 |
122042
|
| 219100 |
Cutis laxa, recessive, type I |
4015 |
LOX lysyl oxidase preproprotein |
chr5 | 106435957.5 | 136435957.5 |
10516
|
| 220400 |
Jervell and Lange-Nielsen syndrome |
3753 |
KCNE1 potassium voltage-gated channel, Isk-related |
chr21 | 16944323 | 46944323 |
3784
|
| 221770 |
Polycystic lipomembranous osteodysplasia with sclerosing leukenencephalophathy |
7305 |
TYROBP TYRO protein tyrosine kinase binding protein |
chr19 | 26089140 | 56089140 |
54209
|
| 223100 |
Hypolactasia, adult type |
3938 |
LCT lactase-phlorizin hydrolase preproprotein |
chr2 | 121404048 | 151404048 |
4175
|
| 224900 |
Ectodermal dysplasia, hypohidrotic, autosomal recessive |
10913 |
EDAR ectodysplasin A receptor |
chr2 | 93988934 | 123988934 |
128178
|
| 225500 |
Ellis-van Creveld syndrome |
2121 |
EVC Ellis van Creveld syndrome protein |
chr4 | 0 | 30000000 |
132884
|
| 226650 |
EBD, generalized atrophic benign |
1308 |
COL17A1 alpha 1 type XVII collagen |
chr10 | 90806201.5 | 120806201.5 |
3691
3909
3914
3918
|
| 226700 |
Epidermolysis bullosa, Herlitz junctional type |
3909 |
LAMA3 laminin alpha 3 subunit isoform 2 |
chr18 | 4747808 | 34747808 |
3914
3918
|
| 226730 |
Epidermolysis bullosa, junctional, with pyloric atresia |
3655 |
ITGA6 integrin alpha chain, alpha 6 |
chr2 | 158155068.5 | 188155068.5 |
3691
|
| 227300 |
Combined factor V and VIII deficiency |
3998 |
LMAN1 lectin, mannose-binding, 1 precursor |
chr18 | 40163380 | 70163380 |
90411
|
| 231200 |
Bernard-Soulier syndrome |
2811 |
GP1BA platelet glycoprotein Ib alpha polypeptide |
chr17 | 0 | 30000000 |
2812
|
| 231680 |
Glutaricaciduria, type IIA |
2108 |
ETFA electron transfer flavoprotein, alpha |
chr15 | 59343369 | 89343369 |
2109
2110
|
| 236670 |
Walker-Warburg syndrome |
2218 |
FCMD fukutin |
chr9 | 90446984 | 120446984 |
10585
|
| 242100 |
Ichthyosiform erythroderma, congenital |
242 |
ALOX12B arachidonate 12-lipoxygenase, 12R type |
chr17 | 0 | 30000000 |
7051
59344
|
| 244400 |
Kartagener syndrome |
1767 |
DNAH5 dynein, axonemal, heavy polypeptide 5 |
chr5 | 0 | 30000000 |
8701
27019
|
| 248200 |
Fundus flavimaculatus |
24 |
ABCA4 ATP-binding cassette, sub-family A member 4 |
chr1 | 79234717.5 | 109234717.5 |
54714
|
| 248310 |
Plasmodium falciparum parasitemia, intensity of |
948 |
CD36 CD36 antigen |
chr7 | 64934410.5 | 94934410.5 |
2995
4843
|
| 251880 |
Mitochondrial DNA-depletion syndrome, hepatocerebral form |
1716 |
DGUOK deoxyguanosine kinase isoform c precursor |
chr2 | 59075660 | 89075660 |
7084
8803
|
| 252010 |
Complex I deficiency |
4719 |
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, |
chr2 | 191829161 | 221829161 |
4720
4723
4724
4726
|
| 252150 |
Molybdenum cofactor deficiency, type A |
4337 |
MOCS1 molybdenum cofactor synthesis-step 1 protein |
chr6 | 24992702.5 | 54992702.5 |
4338
10243
|
| 254500 |
Multiple myeloma |
595 |
CCND1 cyclin D1 |
chr11 | 54170246.5 | 84170246.5 |
3981
|
| 254780 |
Epilepsy, myoclonic, Lafora type |
7957 |
EPM2A laforin isoform b |
chr6 | 131043425 | 161043425 |
378884
|
| 256000 |
Leigh syndrome |
617 |
BCS1L BCS1-like |
chr2 | 204352414.5 | 234352414.5 |
1355
4722
4723
4724
4728
6389
6834
374291
|
| 256450 |
Persistent hyperinsulinemic hypoglycemia of infancy |
3767 |
KCNJ11 potassium inwardly-rectifying channel J11 |
chr11 | 2365627.5 | 32365627.5 |
6833
|
| 256700 |
Neuroblastoma |
4830 |
NME1 non-metastatic cells 1, protein (NM23A) |
chr17 | 31591109.5 | 61591109.5 |
8929
|
| 258100 |
Oguchi disease-1 |
6011 |
GRK1 rhodopsin kinase |
chr13 | 84142980 | 114142980 |
6295
|
| 259420 |
Osteogenesis imperfecta, type III |
1277 |
COL1A1 alpha 1 type I collagen preproprotein |
chr17 | 30625867 | 60625867 |
1278
|
| 259500 |
Osteosarcoma |
5925 |
RB1 retinoblastoma 1 |
chr13 | 32864128.5 | 62864128.5 |
11200
|
| 259700 |
Osteopetrosis, recessive |
1186 |
CLCN7 chloride channel 7 |
chr16 | 0 | 30000000 |
10312
28962
|
| 260350 |
Pancreatic cancer, 1 |
675 |
BRCA2 breast cancer 2, early onset |
chr13 | 16829752 | 46829752 |
3845
7157
7873
|
| 261100 |
Megaloblastic anemia-1 |
8029 |
CUBN cubilin |
chr10 | 2059374.5 | 32059374.5 |
81693
|
| 261515 |
D-bifunctional protein deficiency |
30 |
ACAA1 acetyl-Coenzyme A acyltransferase 1 |
chr3 | 23146535.5 | 53146535.5 |
3295
|
| 261550 |
Persistent Mullerian duct syndrome |
268 |
AMH anti-Mullerian hormone |
chr19 | 0 | 30000000 |
269
|
| 264350 |
Pseudohypoaldosteronism, type I |
6337 |
SCNN1A sodium channel, nonvoltage-gated 1 alpha |
chr12 | 0 | 30000000 |
6338
6340
|
| 265120 |
Pulmonary alveolar proteinosis |
1439 |
CSF2RB colony stimulating factor 2 receptor, beta, |
chr22 | 19554710 | 49554710 |
6439
6440
|
| 266500 |
Refsum disease |
5191 |
PEX7 peroxisomal biogenesis factor 7 |
chr6 | 122230926.5 | 152230926.5 |
5264
|
| 266510 |
Refsum disease, infantile form |
5189 |
PEX1 peroxisome biogenesis factor 1 |
chr7 | 76781910.5 | 106781910.5 |
5828
55670
|
| 266600 |
Crohn disease |
9231 |
DLG5 discs large homolog 5 |
chr10 | 64260569 | 94260569 |
64127
|
| 267430 |
Renal tubular dysgenesis |
183 |
AGT angiotensinogen preproprotein |
chr1 | 212149476 | 242149476 |
185
1636
5972
|
| 268000 |
Retinitis pigmentasa, AR, without hearing loss |
1258 |
CNGB1 cyclic nucleotide gated channel beta 1 |
chr16 | 41517129.5 | 71517129.5 |
1406
6017
7399
10002
10461
|
| 268220 |
Rhabdomyosarcoma, alveolar |
2308 |
FOXO1A forkhead box O1A |
chr13 | 25085004 | 55085004 |
5077
5081
|
| 275000 |
Graves disease |
1493 |
CTLA4 cytotoxic T-lymphocyte-associated protein 4 |
chr2 | 189560606 | 219560606 |
2638
7253
|
| 276300 |
Turcot syndrome with glioblastoma |
324 |
APC adenomatosis polyposis coli |
chr5 | 97163104 | 127163104 |
4292
5395
|
| 277580 |
Shah-Waardenburg syndrome, |
1908 |
EDN3 endothelin 3 isoform 1 preproprotein |
chr20 | 32435964 | 62435964 |
1910
6663
|
| 300009 |
Dent disease |
1184 |
CLCN5 chloride channel 5 |
chrX | 34548764 | 64548764 |
4952
|
| 303700 |
Colorblindness, blue monochromatic |
2652 |
OPN1MW opsin 1 (cone pigments), medium-wave-sensitive |
chrX | 124824264 | 154824264 |
5956
|
| 310200 |
Becker muscular dystrophy modifier |
1756 |
DMD dystrophin Dp116 isoform |
chrX | 16092851.5 | 46092851.5 |
4618
|
| 312750 |
Rett syndrome |
4204 |
MECP2 methyl CpG binding protein 2 |
chrX | 124824264 | 154824264 |
6792
|
| 600101 |
Deafness, autosomal dominant 2 |
2707 |
GJB3 connexin 31 |
chr1 | 19919862.5 | 49919862.5 |
9132
|
| 600263 |
H. pylori infection, susceptibility to |
3459 |
IFNGR1 interferon gamma receptor 1 |
chr6 | 122571508.5 | 152571508.5 |
5803
|
| 600669 |
Epilepsy, generalized idiopathic |
785 |
CACNB4 calcium channel, voltage-dependent, beta 4 |
chr2 | 137650905.5 | 167650905.5 |
4200
|
| 600794 |
Spinal muscular atrophy, distal, with upper limb predominance |
2617 |
GARS glycyl-tRNA synthetase |
chr7 | 15427327.5 | 45427327.5 |
26580
|
| 600802 |
Severe combined immunodeficiency, T-cell negative, B-cell/natural killer cell-positive type |
915 |
CD3D CD3D antigen, delta polypeptide (TiT3 complex) |
chr11 | 102716809 | 132716809 |
3575
|
| 600807 |
Asthma, susceptibility to |
240 |
ALOX5 arachidonate 5-lipoxygenase |
chr10 | 30225437 | 60225437 |
3135
3593
3596
7124
7356
7941
51131
117156
|
| 601386 |
Deafness, autosomal recessive 12 |
491 |
ATP2B2 plasma membrane calcium ATPase 2 isoform b |
chr3 | 0 | 30000000 |
64072
|
| 601457 |
Severe combined immunodeficiency, B cell-negative |
5896 |
RAG1 recombination activating gene 1 |
chr11 | 21552996 | 51552996 |
5897
|
| 601462 |
Myasthenic syndrome, slow-channel congenital |
1134 |
CHRNA1 cholinergic receptor, nicotinic, alpha |
chr2 | 160446493.5 | 190446493.5 |
1140
1144
1145
|
| 601544 |
Deafness, autosomal dominant 3 |
2706 |
GJB2 gap junction protein, beta 2, 26kDa (connexin |
chr13 | 4661379.5 | 34661379.5 |
10804
|
| 601626 |
Leukemia, acute myelogenous |
861 |
RUNX1 runt-related transcription factor 1 isoform b |
chr21 | 16944323 | 46944323 |
1050
2322
3815
4026
4291
4869
6455
8021
8028
8301
8833
23365
26511
54904
64324
|
| 601665 |
Obesity, mild, early-onset |
154 |
ADRB2 adrenergic, beta-2-, receptor, surface |
chr5 | 133187208 | 163187208 |
155
181
4159
4160
5167
5468
6492
7350
7351
7352
8431
9607
51738
|
| 601675 |
Trichothiodystrophy |
2068 |
ERCC2 excision repair cross-complementing rodent |
chr19 | 33811651 | 63811651 |
404672
|
| 601680 |
Arthrogryposis multiplex congenita, distal, type 2B |
7136 |
TNNI2 troponin I, skeletal, fast |
chr11 | 0 | 30000000 |
7140
|
| 602080 |
Paget disease of bone |
8792 |
TNFRSF11A tumor necrosis factor receptor superfamily, |
chr18 | 43173406 | 73173406 |
8878
|
| 602089 |
Hemangioma, capillary infantile |
2324 |
FLT4 fms-related tyrosine kinase 4 isoform 2 |
chr5 | 150857866 | 180857866 |
3791
|
| 602390 |
Hemochromatosis, type 2 |
57817 |
HAMP hepcidin antimicrobial peptide |
chr19 | 25466552.5 | 55466552.5 |
148738
|
| 602475 |
Ossification of posterior longitudinal ligament of spine |
1291 |
COL6A1 collagen, type VI, alpha 1 precursor |
chr21 | 16944323 | 46944323 |
5167
|
| 602522 |
Bartter syndrome, infantile, with sensorineural deafness |
1187 |
CLCNKA chloride channel Ka |
chr1 | 1099939.5 | 31099939.5 |
1188
7809
|
| 602722 |
Renal tubular acidosis, distal, autosomal recessive |
6521 |
SLC4A1 solute carrier family 4, anion exchanger, member |
chr17 | 24689555.5 | 54689555.5 |
50617
|
| 603075 |
Macular degeneration, age-related, 1 |
3075 |
CFH complement factor H isoform b precursor |
chr1 | 178377511 | 208377511 |
59338
83872
|
| 603554 |
Omenn syndrome |
5896 |
RAG1 recombination activating gene 1 |
chr11 | 21552996 | 51552996 |
5897
64421
|
| 603896 |
Leukoencephalopathy with vanishing white matter |
1967 |
EIF2B1 eukaryotic translation initiation factor 2B, |
chr12 | 102449811 | 132449811 |
8890
8891
8892
8893
|
| 603932 |
Intervertebral disc disease, susceptibility to |
1298 |
COL9A2 alpha 2 type IX collagen |
chr1 | 25443954 | 55443954 |
1299
8483
|
| 604219 |
Cataract, congenital |
4284 |
MIP major intrinsic protein of lens fiber |
chr12 | 40132997 | 70132997 |
8419
|
| 604233 |
Epilepsy, generalized, with febrile seizures plus |
2566 |
GABRG2 gamma-aminobutyric acid A receptor, gamma 2 |
chr5 | 146485133 | 176485133 |
6323
6324
|
| 604367 |
Diabetes mellitus, insulin-resistant, with acanthosis nigricans and hypertension |
5468 |
PPARG peroxisome proliferative activated receptor |
chr3 | 0 | 30000000 |
5506
|
| 604370 |
Epithelial ovarian cancer, somatic |
4978 |
OPCML opioid binding protein/cell adhesion |
chr11 | 104452384 | 134452384 |
5290
|
| 604571 |
Bare lymphocyte syndrome, type I |
6891 |
TAP2 transporter 2, ATP-binding cassette, sub-family |
chr6 | 17909298.5 | 47909298.5 |
6892
|
| 604772 |
Ventricular tachycardia, stress-induced polymorphic |
845 |
CASQ2 cardiac calsequestrin 2 |
chr1 | 100989553.5 | 130989553.5 |
6262
|
| 604931 |
Cortisone reductase deficiency |
3290 |
HSD11B1 11-beta-hydroxysteroid dehydrogenase 1 |
chr1 | 191281471.5 | 221281471.5 |
9563
|
| 605074 |
Renal cell carcinoma, papillary, 1 |
4233 |
MET met proto-oncogene precursor |
chr7 | 100981609 | 130981609 |
5546
7030
|
| 605253 |
Neuropathy, congenital hypomyelinating, 1 |
1959 |
EGR2 early growth response 2 protein |
chr10 | 49244383.5 | 79244383.5 |
4359
|
| 605462 |
Basal cell carcinoma, somatic |
5727 |
PTCH patched |
chr9 | 80319473 | 110319473 |
8643
|
| 605899 |
Glycine encephalopathy |
275 |
AMT aminomethyltransferase (glycine cleavage system |
chr3 | 34432431.5 | 64432431.5 |
2653
2731
|
| 606054 |
Propionicacidemia |
5095 |
PCCA propionyl-Coenzyme A carboxylase, alpha |
chr13 | 84142980 | 114142980 |
5096
|
| 606176 |
Diabetes mellitus, neonatal-onset |
2645 |
GCK glucokinase isoform 3 |
chr7 | 28964463.5 | 58964463.5 |
3767
|
| 606657 |
Glaucoma, normal tension, susceptibility to |
4976 |
OPA1 optic atrophy 1 isoform 1 |
chr3 | 169505740 | 199505740 |
10133
|
| 606690 |
Lymphangioleiomyomatosis |
7248 |
TSC1 tuberous sclerosis 1 protein isoform 2 |
chr9 | 108429268 | 138429268 |
7249
|
| 606764 |
Gastrointestinal stromal tumor, somatic |
3815 |
KIT v-kit Hardy-Zuckerman 4 feline sarcoma viral |
chr4 | 40405380 | 70405380 |
5156
|
| 606904 |
Epilepsy, juvenile myoclonic |
785 |
CACNB4 calcium channel, voltage-dependent, beta 4 |
chr2 | 137650905.5 | 167650905.5 |
1181
2554
|
| 607174 |
Meningioma |
4330 |
MN1 meningioma 1 |
chr22 | 11496270.5 | 41496270.5 |
4771
5728
|
| 607208 |
Myoclonic epilepsy, severe, of infancy, 607208 |
2566 |
GABRG2 gamma-aminobutyric acid A receptor, gamma 2 |
chr5 | 146485133 | 176485133 |
6323
|
| 607554 |
Atrial fibrillation, familial |
3784 |
KCNQ1 potassium voltage-gated channel, KQT-like |
chr11 | 0 | 30000000 |
9992
|
| 607748 |
Familial hypercholanemia |
570 |
BAAT bile acid Coenzyme A: amino acid |
chr9 | 86208752.5 | 116208752.5 |
9414
|
| 607785 |
Leukemia, juvenile myelomonocytic |
4763 |
NF1 neurofibromin |
chr17 | 11585876 | 41585876 |
5781
23092
|
| 607948 |
Tuberculosis, susceptibility to |
3458 |
IFNG interferon, gamma |
chr12 | 51837530.5 | 81837530.5 |
6556
|
| 608161 |
Foveomacular dystrophy, adult-onset, with choroidal neovascularization |
5961 |
RDS retinal degeneration slow protein |
chr6 | 27786030 | 57786030 |
7439
|
| 608930 |
Myasthenic syndrome, fast-channel congenital |
1134 |
CHRNA1 cholinergic receptor, nicotinic, alpha |
chr2 | 160446493.5 | 190446493.5 |
1144
1145
|
| 608931 |
Myasthenic syndrome, congenital, associated with acetylcholine receptor deficiency |
1140 |
CHRNB1 nicotinic acetylcholine receptor beta subunit |
chr17 | 0 | 30000000 |
1145
5913
|
| 609135 |
Aplastic anemia |
3458 |
IFNG interferon, gamma |
chr12 | 51837530.5 | 81837530.5 |
7015
|
| 609192 |
Loeys-Dietz syndrome |
7046 |
TGFBR1 transforming growth factor, beta receptor I |
chr9 | 83969092 | 113969092 |
7048
|